News tagged with neuronal ceroid

Transplanted human stem cells prolong survival in mouse model of rare brain disease

A new study finds substantial improvement in a mouse model of a rare, hereditary neurodegenerative disease after transplantation of normal human neural stem cells. The research findings, published by Cell Press in the September ...

Medicine & Health / Medical research

created Sep 03, 2009 | popularity not rated yet | comments 0




Search results for neuronal ceroid


Hope for children with rare genetic defect

To date, there is no therapy for Batten disease. Patients pass away in their teens or twenties. Four years ago, the working group lead by Dr. Mika Ruonala at Goethe University, Frankfurt, Germany started to ...

Medicine & Health / Medical research

created Apr 19, 2011 | popularity 4 / 5 (1) | comments 0

Mutated gene found in dog disease the same in humans, researchers find

University of Missouri researchers believe both man and animal will benefit from their discovery that the same gene mutation found in Tibetan Terrier dogs can also be found in a fatal human neurological disorder ...

Biology / Biotechnology

created Apr 18, 2011 | popularity not rated yet | comments 1

OHSU Doernbecher Children's Hospital conducts second phase of landmark Batten study

Oregon Health & Science University Doernbecher Children's Hospital will lead the next phase of a landmark clinical trial to further assess the safety and preliminary effectiveness of purified human neural stem cells (HuCNS-SC) ...

Medicine & Health / Medical research

created Oct 29, 2010 | popularity not rated yet | comments 0

Researchers find gene responsible for neurodegenerative disease in dogs, possibly in humans

(PhysOrg.com) -- A North Carolina State University researcher has helped to locate and identify a gene responsible for a fatal neurodegenerative disease that affects American Staffordshire terriers. This same gene may be ...

Medicine & Health / Genetics

created Aug 23, 2010 | popularity 5 / 5 (3) | comments 0 | with audio podcast

Yeast mimics severity of mutations leading to fatal childhood illness

Scientists report that human gene mutations expressed in yeast cells can predict the severity of Batten Disease, a fatal nervous system disorder that begins during childhood. The new study published in Disease Models & Me ...

Biology /

created Dec 22, 2008 | popularity not rated yet | comments 0

Researchers identify tumor suppressor that manages cellular cleaning and recycling proceses

Researchers at the University of Southern California (USC) have identified a specific tumor suppressor that manages membrane traffic routes for cellular cleaning and recycling.

Biology /

created Jul 03, 2008 | popularity 4.5 / 5 (2) | comments 0

Gene therapy slows progression of Batten Disease

Gene therapy that helps defective brain cells get rid of "garbage" appears both safe and effective at slowing down Batten disease, according to promising findings from NewYork-Presbyterian Hospital/Weill Cornell Medical Center.

Medicine & Health / Diseases, Conditions, Syndromes

created Jun 02, 2008 | popularity 4.3 / 5 (3) | comments 0

Gene therapy slows progression of fatal neurodegenerative disease in children

Gene therapy to replace the faulty CLN2 gene, which causes a neurodegenerative disease that is fatal by age 8-12 years, was able to slow significantly the rate of neurologic decline in treated children, according to a paper ...

Medicine & Health / Genetics

created May 13, 2008 | popularity not rated yet | comments 0


List of search results for neuronal ceroid